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KMID : 0371320090770040287
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Journal of the Korean Surgical Society
2009 Volume.77 No. 4 p.287 ~ p.290
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Pancreatic Cyst in von Hippel-Lindau Disease
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Sohn Bo-Sung
Cho Chung-Eun
Park Il-Young
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Abstract
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The von Hippel-Lindau (VHL) disease is an autosomal dominant disorder by germline mutation of VHL tumor suppressor gene. The affected patients mainly develop cancers of the central nervous system, renal cell carcinoma, pheochromocytoma, and pancreatic cysts. Pancreatic involvement was observed 12∼77% in VHL patients and included true cysts, serous cystadenomas, and neuroendocrine tumors. We experienced two cases of pancreatic cyst of the von Hippel-Lindau disease and reviewed associated literatures.
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KEYWORD
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von Hippel-Lindau disease, Pancreatic cyst
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